A case of Kasabach-Merritt Syndrome in a nine-month-old; a rare complication of haemangioma in the young

Authors

  • Hafiz Khalid Pervaiz Department of Vascular Surgery, Combined Military Hospital, Lahore, Pakistan
  • Usman Jamil Mughal Department of Vascular and Endovascular Surgery, Combined Military Hospital, Lahore, Pakistan
  • Izza Ali Rai Department of Vascular Surgery, Combined Military Hospital, Lahore, Pakistan
  • Mumtaz Touseef Department of Medicine, Combined Military Hospital, Lahore, Pakistan
  • Aliezeh Fatima Rai Department of Vascular Surgery, Combined Military Hospital, Lahore, Pakistan

DOI:

https://doi.org/10.47391/JPMA.11607

Keywords:

Haemangioma, Vincristine, Consumptive coagulopathy, KMP, Thrombocytopenia, Haemangioendothelioma

Abstract

Kasabach-Merritt Phenomenon (KMP) is a life-threatening consumptive coagulopathy that commonly occurs in infants and young children. It is a combination of an enlarging vascular lesion, thrombocytopenia, microangiopathic haemolytic anaemia, and hypofibrinogemia. The case of a nine-month-old child who presented with a tuft haemangioma leading to the clinical features of KMP is presented. The investigation which was performed and pharmacological treatment initiated at different stages of presentation and the characteristic response to treatment are also discussed.

Keywords: Haemangioma, Vincristine, Consumptive coagulopathy, KMP, Thrombocytopenia, Haemangioendothelioma.

Published

2025-02-23

How to Cite

Hafiz Khalid Pervaiz, Usman Jamil Mughal, Rai, I. A., Mumtaz Touseef, & Aliezeh Fatima Rai. (2025). A case of Kasabach-Merritt Syndrome in a nine-month-old; a rare complication of haemangioma in the young. Journal of the Pakistan Medical Association, 75(03), 488–491. https://doi.org/10.47391/JPMA.11607

Issue

Section

CASE REPORT