Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report

Authors

  • Faisal Shamim Department of Anaesthesiology, Aga Khan University, Karachi, Pakistan
  • Amber Gulamani Department of Anaesthesiology, Aga Khan University, Karachi, Pakistan
  • Abdullah Nisar Department of Anaesthesiology, Aga Khan University, Karachi, Pakistan
  • Saima Rashid Department of Anaesthesiology, Aga Khan University, Karachi, Pakistan
  • Humayun kaleem Siddiqui Department of Surgery, Aga Khan University, Karachi, Pakistan

DOI:

https://doi.org/10.47391/JPMA.8635

Keywords:

Mucopolysaccharidosis II, Videolaryngoscope, Fibre optic bronchoscope, Difficult airway, Endotracheal intubation, Case report

Abstract

Hunter syndrome (mucopolysaccharidosis type II) has the highest reported prevalence of difficult tracheal intubation among the seven known types of mucopolysaccharidoses. Despite improved difficult airway guidelines and equipment, conventional approaches may fail in some cases. A 10-year-old child with Hunter syndrome, was scheduled for multiple dental extractions. On the first visit, failed intubation was declared as per Difficult Airway Society guidelines in the surgical day-care suite of our institute and the procedure was postponed. The case was then planned to be handled in the main operating room with additional preparation and input from the paediatric otolaryngologist for possible tracheostomy, paediatric intensive care for postoperative need for ventilation, and difficult airway resource faculty for an unconventional approach—videolaryngoscope combined with fibreoptic bronchoscope—which resulted in safe administration of anaesthesia. This case illustrates the importance of meticulous planning in the management of previously failed airway.

Published

2023-10-30

How to Cite

Shamim, F., Gulamani, A., Nisar, A., Rashid, S., & Siddiqui, H. kaleem. (2023). Flexible bronchoscopy combined with videolaryngoscope for tracheal intubation in a child with Hunter syndrome: a case report. Journal of the Pakistan Medical Association, 73(11), 2273–2276. https://doi.org/10.47391/JPMA.8635

Issue

Section

Case Report

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