Intraocular medulloepithelioma: an unusual and challenging entity in paediatric population Authors Uzma Imam Department of Paediatric Oncology, National Institute of Child Health, Karachi, Pakistan Marya Hameed Department of Radiology, National Institute of Child Health, Karachi, Pakistan Irma Anis Department of Paediatrics, Civil Hospital, Karachi, Pakistan Israr Bhutto Department of Ophthalmology, Al Ibrahim Eye Hospital, Karachi, Pakistan Syed Habib Ahmed Department of Paediatric Oncology, National Institute of Child Health, Karachi, Pakistan Attiya Rizvi Department of Ophthalmology, Al Ibrahim Eye Hospital, Karachi, Pakistan Zubair Ahmad Department of Histopathology, Aga Khan University Hospital, Karachi, Pakistan DOI: https://doi.org/10.47391/JPMA.8253 Keywords: Pediatric, Medulloepithelioma, DICER1 associated tumors Abstract Intraocular medulloepithelioma is a rare, congenital tumour of the non-pigmented ciliary epithelium. It most frequently arises from the ciliary body but can also have its origin from the retina, iris and optic nerve. The age when lesion first appears is typically around 2-10 years. Nearly 50-60% of patients having this lesion may also have secondary features such as cataract and neovascular glaucoma. Those with extrascleral medulloepithelioma are at risk for metastasis. Systemic correlation of the tumour with pleuropulmonary blastoma/DICER1 gene is reported in the literature. Here, we report a case of a 15 years old boy with one year history of right eye proptosis and painful red right eye along with decreased vision for one week. He was assessed and operated for cataract elsewhere three years back. ---Continue Downloads Full Text Article Published 2023-11-28 How to Cite Uzma Imam, Marya Hameed, Anis, I., Israr Bhutto, Syed Habib Ahmed, Attiya Rizvi, & Zubair Ahmad. (2023). Intraocular medulloepithelioma: an unusual and challenging entity in paediatric population. Journal of the Pakistan Medical Association, 73(12), 2469–2472. https://doi.org/10.47391/JPMA.8253 More Citation Formats ACM ACS APA ABNT Chicago Harvard IEEE MLA Turabian Vancouver Download Citation Endnote/Zotero/Mendeley (RIS) BibTeX Issue Vol. 73 No. 12 (2023): DECEMBER Section CASE REPORT License Copyright (c) 2023 Journal of the Pakistan Medical Association This work is licensed under a Creative Commons Attribution 4.0 International License.